Aggressive juvenile fibromatosis of the paranasal sinuses: case report and brief review

Table 1 Reported cases of pediatric desmoid fibromatosis of the paranasal sinuses.

Age	Location	Presentation	Pathology	Therapy	Response	Reference
2 year old male	Right maxillary sinus	Nasal obstruction	Aggressive fibromatosis	Surgical resection	Lost to follow up	[1]
14 year old female	Right parotid/mandible	Right facial deformity	Aggressive fibromatosis	Surgical resection (positive margins)	No recurrence at < 1 year	[6]
15 month old male	Nasal cavity/anterior maxilla	Facial deformity	Aggressive fibromatosis	1. Surgical resection (positive margins) 2. Surgical resection (negative margins)	Recurrence in 1 month, no recurrence	[5]
2 year old male	Left maxillary sinus	Nasal deformity	Desmoid fibromatosis	Surgical resection (twice), followed by adjuvant tamoxifen	No recurrence at 2 years	[4]

Conley et al. [2] reported a series of 40 different cases, three cases between the ages 1–10. One of these cases involved the ethmoid sinus.
Fu [3] reported two cases of juvenile fibromatosis ages 2 and 10. One of these cases involved the maxillary sinus.

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