Table 1 Classification of mast cell activation disease (modified from [2–4]).
Mast cell activation disease (MCAD) | |
|---|---|
Mast cell activation syndrome (MCAS) | |
Systemic mastocytosis (SM) defined by the WHO criteria | • Indolent systemic mastocytosis • Isolated bone marrow mastocytosis • Smoldering systemic mastocytosis • Systemic mastocytosis with an associated clonal hematologic non-mast cell lineage disease • Aggressive systemic mastocytosis |
Mast cell leukemia (MCL) |