Characteristics | Number of patients | Percentage |
---|---|---|
Median age, years (range) | 50 (16–75) | |
Sex | ||
Male | 14 | 67 |
Female | 7 | 33 |
PS | ||
0–1 | 12 | 57 |
2–4 | 9 | 43 |
Initial presentation | ||
Fever | 20 | 95 |
General weakness | 1 | 5 |
DOE | 1 | 5 |
Lt. neck swelling | 1 | 5 |
B symptom (+) | 20 | 95 |
Hepatomegaly | 13 | 62 |
Splenomegaly | 17 | 81 |
Pancytopenia | 11 | 52 |
LFT abnormality | 20 | 95 |
DIC | 9 | 43 |
AKI | 4 | 19 |
LDH > normal | 20 | 95 |
Stage IV | 21 | 100 |
IPI score | ||
Low | 1 | 5 |
Low intermediate | 7 | 33 |
High intermediate | 7 | 33 |
High | 6 | 29 |
Nodal involvement | 7 | 33 |
Extranodal involvement | 7 | 33 |
EBV ISH (+) | 17 | 81 |
HLH feature | 16 | 76 |
PET uptake at diagnosis | 9 | 43 |